Hcm Risk Kids Calculator

HCM Risk Equation:

\[ Probability (\%) = 1 - 0.95^{\exp(Prognostic\ Index)} \] \[ Prognostic\ Index = 0.2171364 \times MWT\ (z-score) - 0.012112 \times MWT^2\ (z-score^2) + 0.220196 \times LA\ diameter\ (z-score) + 0.0678578 \times MLVOTG\ (mm\ Hg) + 0.701063 \times FHSCD\ (0/1) + 0.5366 \times NSVT\ (0/1) + 0.995956 \times Unexplained\ syncope\ (0/1) \]

MWT (z-score):

LA diameter (z-score):

MLVOTG (mm Hg):

FHSCD:

NSVT:

Unexplained syncope:

Probability (%):

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1. What is the HCM Risk Kids Calculator?

The HCM Risk Kids Calculator estimates the probability of sudden cardiac death (SCD) in pediatric patients with hypertrophic cardiomyopathy (HCM). It uses a prognostic index based on multiple clinical variables.

2. How Does the Calculator Work?

The calculator uses the following equations:

Where:

MWT — Maximum wall thickness (z-score)
LA diameter — Left atrial diameter (z-score)
MLVOTG — Maximum left ventricular outflow tract gradient (mm Hg)
FHSCD — Family history of sudden cardiac death (0 or 1)
NSVT — Non-sustained ventricular tachycardia (0 or 1)
Unexplained syncope — (0 or 1)

3. Importance of SCD Risk Calculation

Details: Accurate SCD risk estimation is crucial for risk stratification and guiding clinical management in pediatric HCM patients.

4. Using the Calculator

Tips: Enter all required parameters. For binary variables (FHSCD, NSVT, syncope), select 1 for presence and 0 for absence of the risk factor.

5. Frequently Asked Questions (FAQ)

Q1: What population was this calculator validated in?
A: This calculator was developed and validated in pediatric HCM patients.

Q2: What is considered high risk?
A: Risk thresholds should be interpreted in clinical context. Generally, probabilities >5-10% may warrant closer monitoring or intervention.

Q3: How often should risk be reassessed?
A: Risk should be reassessed periodically as clinical parameters may change over time.

Q4: Are there limitations to this calculator?
A: The calculator may be less accurate in patients with extreme values or rare clinical presentations.

Q5: Should this be the sole factor in clinical decision making?
A: No, this should be used in conjunction with comprehensive clinical assessment.